Menene zazzabi na iyali (FMF)?

Menene zazzabi na iyali (FMF)?
Familial Mediterranean Fever cuta ce ta gado wacce ke bayyana kanta tare da gunaguni na ciwon ciki da zazzabi a hare-hare kuma ana iya rikicewa tare da m appendicitis.

Familial Mediterranean Fever cuta ce ta gado wacce ke bayyana kanta tare da gunaguni na ciwon ciki da zazzabi a hare-hare kuma ana iya rikicewa tare da m appendicitis.

Menene Cutar FMF (Familial Mediterranean Fever)?

Ana yawan ganin zazzabin Familial Mediterranean musamman a ƙasashen da ke kan iyaka da Bahar Rum. Ya zama ruwan dare a Turkiyya, Arewacin Afirka, Armeniyawa, Larabawa da Yahudawa. An fi saninta da Familial Mediterranean Fever (FMF).

Cutar ta FMF tana da ciwon ciki, zafi da jin zafi a cikin haƙarƙarin haƙarƙari (plevititis) da ciwon haɗin gwiwa da kumburi (arthritis) saboda kumburi na ciki na ciki, wanda ya sake faruwa a cikin hare-hare kuma yana iya wuce kwanaki 3-4. Wani lokaci, ana iya ƙara jajayen fata a gaban ƙafafu zuwa hoton. Gabaɗaya, waɗannan korafe-korafen na iya tafiya da kansu a cikin kwanaki 3-4, ko da ba a ba da magani ba. Hare-hare da ake ta yi na sa sunadaran da ake kira amyloid ya taru a jikinmu na tsawon lokaci. Amyloid yakan taru a cikin kodan, inda zai iya haifar da gazawar koda. A ɗan ƙarami, yana iya tarawa a cikin ganuwar jijiyoyin jini kuma ya haifar da vasculitis.

Sakamakon binciken asibiti yana faruwa ne sakamakon maye gurbi a cikin kwayar halittar da ake kira pyrin. Ana daukar kwayar cutar ta kwayoyin halitta. Yayin da kasancewar kwayoyin cuta guda biyu tare suna haifar da cutar, ɗaukar kwayar cutar ba ta haifar da cutar. Ana kiran waɗannan mutane "masu ɗaukar kaya".

Menene Alamomin Familial Mediterranean Fever (FMF)?

Familial Mediterranean Fever (FMF) cuta ce ta kwayoyin halitta da aka saba gani a yankin Bahar Rum. Alamun FMF na iya bayyana kamar zazzabi mai zafi, zafi mai tsanani na ciki, ciwon haɗin gwiwa, ciwon kirji, da gudawa. Ciwon ciki yana farawa ba zato ba tsammani kuma yakan wuce daga saoi 12 zuwa 72, yayin da ciwon ciki yana da hali mai kaifi, musamman a kusa da cibiya. Ana jin ciwon haɗin gwiwa musamman a manyan gidajen abinci kamar gwiwa da ƙafafu, yayin da ciwon ƙirji zai iya faruwa a gefen hagu. Ana iya ganin gudawa yayin harin kuma yawanci ana iya jin shi na ɗan gajeren lokaci.

Yaya ake gano cutar zazzabin Familial Mediterranean (FMF)?

Ana yin ganewar asali ne bisa binciken asibiti, tarihin iyali, binciken bincike da gwaje-gwajen dakin gwaje-gwaje. Waɗannan gwaje-gwajen, tare da haɓakar leukocyte mai girma, haɓaka haɓaka, haɓakar CRP da haɓakar fibrinogen, suna tallafawa gano cutar zazzabin Familial Mediterranean. Amfanin gwajin kwayoyin halitta a cikin marasa lafiya yana da iyaka saboda maye gurbin da aka gano har zuwa yau ana iya samun tabbatacce a kashi 80% na marasa lafiya na Familial Mediterranean Fever. Duk da haka, nazarin kwayoyin halitta na iya zama da amfani a lokuta masu ban mamaki.

Shin zai yiwu a yi maganin cutar zazzabin Bahar Rum (FMF)?

An ƙaddara cewa maganin colchicine na Familial Mediterranean Fever yana hana hare-hare da ci gaba da amyloidosis a cikin adadi mai yawa na marasa lafiya. Duk da haka, amyloidosis har yanzu yana da matsala mai tsanani a cikin marasa lafiya waɗanda ba su bi jiyya ba ko kuma sun jinkirta fara colchicine. Maganin Colchicine yakamata ya kasance tsawon rai. An san cewa maganin colchicine amintaccen magani ne, dacewa da mahimmanci ga marasa lafiya da zazzabin Bahar Rum. Ana ba da shawarar yin amfani da shi ko da majiyyaci yana da ciki. Ba a nuna Colchicine yana da cutarwa ga jariri ba. Duk da haka, ana ba da shawarar cewa majinyata masu ciki masu fama da zazzabi na iyali su sha amniocentesis kuma su bincika tsarin kwayoyin halitta na tayin.